Indian Journal of Dental Research

CASE REPORT
Year
: 2008  |  Volume : 19  |  Issue : 3  |  Page : 264--266

Partial expression of Papillon-Lefèvre Syndrome


Shaila V Kothiwale, Setu Mathur 
 Department of Periodontics, KLES'S Institute of Dental Sciences, Belgaum, India

Correspondence Address:
Shaila V Kothiwale
Department of Periodontics, KLES«SQ»S Institute of Dental Sciences, Belgaum
India

Papillon-Lefθvre Syndrome (PLS) is a rare autosomal recessive trait, which is transmitted with an estimated frequency of one to four per million individuals. It is characterized by palmar plantar keratosis and severe early-onset periodontitis affecting both deciduous and permanent dentition. In this report, we present clinical, microbiological and leukocyte function test findings of a thirty-five year-old patient with symptoms typical of Papillon-Lefθvre Syndrome except for premature loss of deciduous and permanent dentition. The patient exhibited palmar plantar keratosis and an isolated, moderately deep periodontal pocket in the third quadrant. No anaerobic bacteria were isolated from the plaque culture. The neutrophil function test revealed defective chemotaxis and phagocytosis while intracellular killing and respiratory burst were normal.


How to cite this article:
Kothiwale SV, Mathur S. Partial expression of Papillon-Lefèvre Syndrome.Indian J Dent Res 2008;19:264-266


How to cite this URL:
Kothiwale SV, Mathur S. Partial expression of Papillon-Lefèvre Syndrome. Indian J Dent Res [serial online] 2008 [cited 2021 Nov 30 ];19:264-266
Available from: https://www.ijdr.in/article.asp?issn=0970-9290;year=2008;volume=19;issue=3;spage=264;epage=266;aulast=Kothiwale;type=0